{"id":9103,"date":"2018-06-21T12:41:34","date_gmt":"2018-06-21T12:41:34","guid":{"rendered":"http:\/\/fefac.cat\/empresarial\/?p=9103"},"modified":"2018-06-21T12:41:34","modified_gmt":"2018-06-21T12:41:34","slug":"21-de-juny-dia-internacional-de-lesclerosi-later","status":"publish","type":"post","link":"https:\/\/fefac.cat\/empresarial\/21-de-juny-dia-internacional-de-lesclerosi-later\/","title":{"rendered":"21 de juny: Dia Internacional de l&#8217;Esclerosi Lateral Amiotr\u00f2fica (ELA)"},"content":{"rendered":"<p>Avui, 21 de juny, &eacute;s el <strong>Dia Internacional de l&#39;Esclerosi Lateral Amiotr&ograve;fica (ELA)<\/strong>, la malaltia neuromuscular m&eacute;s freq&uuml;ent i la tercera malaltia neurodegenerativa m&eacute;s com&uacute;, despr&eacute;s de la dem&egrave;ncia i el Parkinson. Segons dades de la Societat Espanyola de Neurologia (SEN) cada any es diagnostiquen uns 900 nous casos al nostre pa&iacute;s d&#39;aquesta malaltia que afectar&agrave; a un de cada 400-800 espanyols al llarg de la seva vida.<\/p>\n<p>Malgrat ser una malaltia relativament freq&uuml;ent, la seva alta mortalitat fa que el nombre d&#39;afectats sigui relativament baix, ja que la xifra de defuncions anuals &eacute;s similar a la dels nous casos diagnosticats. La Societat Espanyola de Neurologia estima que actualment existirien al voltant de <strong>3.000 afectats a Espanya.<\/strong><\/p>\n<p>Aquesta malaltia que apareix generalment de forma espor&agrave;dica, ja que nom&eacute;s en un 5-10% dels casos existeixen antecedents familiars, tamb&eacute; t&eacute; una etiologia incerta, ja que els primers s&iacute;mptomes acostumen a apar&egrave;ixer quan els pacients tenen seixanta anys (una mica menys en cas de tenir antecedents familiars) i acostuma a ser una mica m&eacute;s freq&uuml;ent en homes, de fet, <strong>ser home i tenir una edat avan&ccedil;ada<\/strong> s&oacute;n els &uacute;nics factors de risc que s&#39;han pogut establir.<\/p>\n<p>No obstant aix&ograve;, tamb&eacute; existeixen estudis que apunten altres <strong>factors<\/strong>:<\/p>\n<ul>\n<li>Ser fumador.<\/li>\n<li>Haver patit alguna infecci&oacute; viral pr&egrave;via.<\/li>\n<li>Haver estat exposat de forma habitual a metalls pesants i\/o pesticides.<\/li>\n<li>Haver realitzat amb assidu&iuml;tat activitats f&iacute;siques intenses, entre d&#39;altres.<\/li>\n<\/ul>\n<p>En tot cas, no sembla que existeixi una explicaci&oacute; &uacute;nica, sin&oacute; una combinaci&oacute; de factors, molts d&#39;ells encara per determinar, els que comportarien <strong>l&#39;aparici&oacute; de la malaltia.<\/strong><\/p>\n<p>Encara que l&#39;ELA &eacute;s una malaltia caracteritzada per l&#39;heterogene&iuml;tat dels seus s&iacute;mptomes i la variabilitat de la seva evoluci&oacute;, presentar <strong>feblesa en les extremitats<\/strong> (60-85% dels casos) o <strong>a la regi&oacute; bulbar<\/strong> (15-40%), aix&iacute; com p&egrave;rdua de for&ccedil;a progressiva, pesadesa, disminuci&oacute; de la massa muscular i enrampades, solen ser les primeres manifestacions de la malaltia. Assenyalar tamb&eacute; que un 5-10% dels pacients presenten una dem&egrave;ncia associada, generalment de tipus frontotemporal.<\/p>\n<p><strong>Nom&eacute;s existeix un tractament aprovat per a aquesta malaltia <\/strong>i el seu efecte i, encara que est&agrave; demostrat, &eacute;s relativament discret. Actualment, el diagn&ograve;stic de la malaltia es demora entre 17 i 20 mesos i els majors retards es produeixen entre les persones entre les quals els primers s&iacute;mptomes s&oacute;n els bulbars.<\/p>\n<p>La Societat Espanyola de Neurologia considera imprescindible <strong>dedicar recursos al desenvolupament i implementaci&oacute; de tractaments<\/strong> dirigits a la prevenci&oacute; i control de la discapacitat d&#39;aquesta malaltia, que figura entre les principals causes de discapacitat del nostre pa&iacute;s i que, a m&eacute;s, t&eacute; un alt cost sociosanitari, al voltant dels 50.000 euros anuals per pacient.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Avui, 21 de juny, &eacute;s el Dia Internacional de l&#39;Esclerosi Lateral Amiotr&ograve;fica (ELA), la malaltia neuromuscular m&eacute;s freq&uuml;ent i la tercera malaltia neurodegenerativa m&eacute;s com&uacute;, despr&eacute;s de la dem&egrave;ncia i [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_et_pb_use_builder":"","_et_pb_old_content":"","_et_gb_content_width":"","footnotes":""},"categories":[18,11,12,13,14,15],"tags":[1079,1127,1137,1456,1704],"class_list":["post-9103","post","type-post","status-publish","format-standard","hentry","category-general","category-fefac","category-afb","category-afet","category-afell","category-agfe","tag-dies-mundials","tag-farmacia","tag-ela","tag-salut","tag-pacient"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.6 - 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